Hemophagocytic lymphohistiocytosis in adults: a key issue in the COVID-19 era

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MetadadosDescriçãoIdioma
Autor(es): dc.creatorPereira, Miguel Augusto Martins-
Autor(es): dc.creatorCosta, Lygia Marina Mendes da-
Autor(es): dc.creatorNascimento, Suelen Brito-
Autor(es): dc.creatorKang, Hye Chung-
Autor(es): dc.creatorGabriel, Adelmo Henrique Daumas-
Data de aceite: dc.date.accessioned2025-08-21T20:10:47Z-
Data de disponibilização: dc.date.available2025-08-21T20:10:47Z-
Data de envio: dc.date.issued2025-06-05-
Data de envio: dc.date.issued2025-06-05-
Data de envio: dc.date.issued2020-
Fonte completa do material: dc.identifierhttps://app.uff.br/riuff/handle/1/38666-
Fonte: dc.identifier.urihttp://educapes.capes.gov.br/handle/capes/1056041-
Descrição: dc.descriptionSim-
Descrição: dc.descriptionHemophagocytic lymphohistiocytosis (HLH) is a syndrome characterized by persistent activation of the mono nuclear phagocytic system, systemic inflammation, and hypercytokinaemia, which can lead to liver failure, “sepsis-like syndrome” and ultimately, to multiple organ failure and death. These disorders can be divided into primary and secondary (or reactive), the first, also known as familial HLH, is a genetic condition of childhood,which affects the function of TCD8 and NK cells, and usually presents in the first year of life. The secondary HLH affects mainly adults and adolescents and, it’s more related to dysregulation of the immune system. In face of the COVID-19 pandemic and several reports of HLH by SARS-CoV-2, it is necessary to discuss the pathophysiology of HLH in adults more clearly. Thus, we present, for the first time, a didactic approach using illustrations and tables, compiling the most recent and relevant information to better understand this entity.-
Formato: dc.formatapplication/pdf-
Idioma: dc.languageen-
Publicador: dc.publisherBritish Infection Association-
Relação: dc.relationCLINICAL INFECTION IN PRACTICE. Livingston: British Infection Association, 2020-. ISSN: 2590-1702-
Direitos: dc.rightsOpen Access-
Direitos: dc.rightsCC-BY-SA-
Palavras-chave: dc.subjectFagocitose-
Palavras-chave: dc.subjectCOVID-19-
Palavras-chave: dc.subjectLinfo-Histiocitose Hemofagocítica-
Palavras-chave: dc.subjectMutação (Genética)-
Palavras-chave: dc.subjectHemophagocytosis-
Palavras-chave: dc.subjectSARS-CoV-2-
Palavras-chave: dc.subjectCOVID-19-
Palavras-chave: dc.subjectHaemophagocytic syndrome-
Palavras-chave: dc.subjectMutations-
Título: dc.titleHemophagocytic lymphohistiocytosis in adults: a key issue in the COVID-19 era-
Tipo de arquivo: dc.typeArtigo de periódico-
Aparece nas coleções:Repositório Institucional da Universidade Federal Fluminense - RiUFF

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