Polycystic Liver Disease: Pathophysiology, Diagnosis and Treatment

Registro completo de metadados
MetadadosDescriçãoIdioma
Autor(es): dc.contributorUniversidade Estadual Paulista (UNESP)-
Autor(es): dc.creatorNorcia, Luiz Fernando-
Autor(es): dc.creatorWatanabe, Erika Mayumi-
Autor(es): dc.creatorHamamoto Filho, Pedro Tadao-
Autor(es): dc.creatorHasimoto, Claudia Nishida-
Autor(es): dc.creatorPelafsky, Leonardo-
Autor(es): dc.creatorOliveira, Walmar Kerche de-
Autor(es): dc.creatorSassaki, Ligia Yukie-
Data de aceite: dc.date.accessioned2025-08-21T15:39:59Z-
Data de disponibilização: dc.date.available2025-08-21T15:39:59Z-
Data de envio: dc.date.issued2023-07-29-
Data de envio: dc.date.issued2023-07-29-
Data de envio: dc.date.issued2021-12-31-
Fonte completa do material: dc.identifierhttp://dx.doi.org/10.2147/HMER.S377530-
Fonte completa do material: dc.identifierhttp://hdl.handle.net/11449/245479-
Fonte: dc.identifier.urihttp://educapes.capes.gov.br/handle/11449/245479-
Descrição: dc.descriptionPolycystic liver disease (PLD) is a clinical condition characterized by the presence of more than 10 cysts in the liver. It is a rare disease Of genetic etiology that presents as an isolated disease or assoc\iated with polycystic kidney disease. Ductal plate malformation, ciliary dysfunction, and changes in cell signaling are the main factors involved in its pathogenesis. Most patients with PLD are asymptomatic, but in 2-5% of cases the disease has disabling symptoms and a significant reduction in quality of life. The diagnosis is based on family history of hepatic and/or renal polycystic disease, clinical manifestations, patient age, and polycystic liver phenotype shown on imaging examinations. PLD treatment has evolved considerably in the last decades. Somatostatin analogues hold promise in controlling disease progression, but liver transplantation remains a unique curative treatment modality.-
Descrição: dc.descriptionSao Paulo State Univ Unesp, Med Sch, Dept Surg, Botucatu, SP, Brazil-
Descrição: dc.descriptionSao Paulo State Univ Unesp, Med Sch, Dept Radiol, Botucatu, SP, Brazil-
Descrição: dc.descriptionSao Paulo State Univ Unesp, Med Sch, Dept Neurol Psychol & Psychiat, Botucatu, SP, Brazil-
Descrição: dc.descriptionSao Paulo State Univ Unesp, Med Sch, Dept Internal Med, Botucatu, SP, Brazil-
Descrição: dc.descriptionSao Paulo State Univ UNESP, Med Sch, Dept Surg, 783 Pedro Delmanto St, BR-18610303 Botucatu, SP, Brazil-
Descrição: dc.descriptionSao Paulo State Univ Unesp, Med Sch, Dept Surg, Botucatu, SP, Brazil-
Descrição: dc.descriptionSao Paulo State Univ Unesp, Med Sch, Dept Radiol, Botucatu, SP, Brazil-
Descrição: dc.descriptionSao Paulo State Univ Unesp, Med Sch, Dept Neurol Psychol & Psychiat, Botucatu, SP, Brazil-
Descrição: dc.descriptionSao Paulo State Univ Unesp, Med Sch, Dept Internal Med, Botucatu, SP, Brazil-
Descrição: dc.descriptionSao Paulo State Univ UNESP, Med Sch, Dept Surg, 783 Pedro Delmanto St, BR-18610303 Botucatu, SP, Brazil-
Formato: dc.format135-161-
Idioma: dc.languageen-
Publicador: dc.publisherDove Medical Press Ltd-
Relação: dc.relationHepatic Medicine-evidence And Research-
???dc.source???: dc.sourceWeb of Science-
Palavras-chave: dc.subjectliver-
Palavras-chave: dc.subjectpolycystic liver disease-
Palavras-chave: dc.subjecthepatomegaly-
Palavras-chave: dc.subjectliver cysts-
Palavras-chave: dc.subjecttherapeutics-
Título: dc.titlePolycystic Liver Disease: Pathophysiology, Diagnosis and Treatment-
Tipo de arquivo: dc.typevídeo-
Aparece nas coleções:Repositório Institucional - Unesp

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