Childhood Sjögren syndrome: Features of an international cohort and application of the 2016 ACR/EULAR classification criteria

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MetadadosDescriçãoIdioma
Autor(es): dc.contributorMayo Clinic-
Autor(es): dc.contributorUniversity of Utah School of Medicine-
Autor(es): dc.contributorThe Children's Hospital of Philadelphia-
Autor(es): dc.contributorThe University of Chicago Medical Center-
Autor(es): dc.contributorDuke University School of Medicine-
Autor(es): dc.contributorMedical University of Gdansk-
Autor(es): dc.contributorUniversity of Missouri-Kansas City-
Autor(es): dc.contributorIrccs Ospedale Pediatrico Bambino Gesù-
Autor(es): dc.contributorInstitute of Rheumatology-
Autor(es): dc.contributorColumbia University Medical Center-
Autor(es): dc.contributorGeorge Washington University School of Medicine and Health Sciences-
Autor(es): dc.contributorNational Institute of Arthritis and Musculoskeletal and Skin Diseases-
Autor(es): dc.contributorUniversity of Texas McGovern Medical School at Houston-
Autor(es): dc.contributorEmory University School of Medicine-
Autor(es): dc.contributorUniversidade Federal do Rio de Janeiro (UFRJ)-
Autor(es): dc.contributorHospital Sant Joan de Déu-
Autor(es): dc.contributorBarcelona-
Autor(es): dc.contributorUniversidade Estadual de Campinas (UNICAMP)-
Autor(es): dc.contributorRiley Hospital for Children at Indiana University Health-
Autor(es): dc.contributorUniversidade Estadual Paulista (UNESP)-
Autor(es): dc.contributorMelbourne and Murdoch Children's Research Institute-
Autor(es): dc.contributorUniversity of Florida-
Autor(es): dc.contributorHospital General Universitario Gregorio Marañón-
Autor(es): dc.contributorHarvard Medical School-
Autor(es): dc.contributorTokyo Metropolitan Tama Medical Center-
Autor(es): dc.contributorUniversity of Iowa-
Autor(es): dc.creatorBasiaga, Matthew L.-
Autor(es): dc.creatorStern, Sara M.-
Autor(es): dc.creatorMehta, Jay J.-
Autor(es): dc.creatorEdens, Cuoghi-
Autor(es): dc.creatorRandell, Rachel L.-
Autor(es): dc.creatorPomorska, Anna-
Autor(es): dc.creatorIrga-Jaworska, Ninela-
Autor(es): dc.creatorIbarra, Maria F.-
Autor(es): dc.creatorBracaglia, Claudia-
Autor(es): dc.creatorNicolai, Rebecca-
Autor(es): dc.creatorSusic, Gordana-
Autor(es): dc.creatorBoneparth, Alexis-
Autor(es): dc.creatorSrinivasalu, Hemalatha-
Autor(es): dc.creatorDizon, Brian-
Autor(es): dc.creatorKamdar, Ankur A.-
Autor(es): dc.creatorGoldberg, Baruch-
Autor(es): dc.creatorKnupp-Oliveira, Sheila-
Autor(es): dc.creatorAntón, Jordi-
Autor(es): dc.creatorMosquera, Juan M.-
Autor(es): dc.creatorAppenzeller, Simone-
Autor(es): dc.creatorO'Neil, Kathleen M.-
Autor(es): dc.creatorProtopapas, Stella A.-
Autor(es): dc.creatorSaad-Magalhães, Claudia-
Autor(es): dc.creatorAkikusa, Jonathan D.-
Autor(es): dc.creatorThatayatikom, Akaluck-
Autor(es): dc.creatorCha, Seunghee-
Autor(es): dc.creatorNieto-González, Juan Carlos-
Autor(es): dc.creatorLo, Mindy S.-
Autor(es): dc.creatorTreemarcki, Erin Brennan-
Autor(es): dc.creatorYokogawa, Naoto-
Autor(es): dc.creatorLieberman, Scott M.-
Data de aceite: dc.date.accessioned2025-08-21T19:42:21Z-
Data de disponibilização: dc.date.available2025-08-21T19:42:21Z-
Data de envio: dc.date.issued2022-04-29-
Data de envio: dc.date.issued2022-04-29-
Data de envio: dc.date.issued2021-07-01-
Fonte completa do material: dc.identifierhttp://dx.doi.org/10.1093/rheumatology/keaa757-
Fonte completa do material: dc.identifierhttp://hdl.handle.net/11449/229166-
Fonte: dc.identifier.urihttp://educapes.capes.gov.br/handle/11449/229166-
Descrição: dc.descriptionObjective: Sjögren syndrome in children is a poorly understood autoimmune disease. We aimed to describe the clinical and diagnostic features of children diagnosed with Sjögren syndrome and explore how the 2016 ACR/EULAR classification criteria apply to this population. Methods: An international workgroup retrospectively collected cases of Sjögren syndrome diagnosed under 18 years of age from 23 centres across eight nations. We analysed patterns of symptoms, diagnostic workup, and applied the 2016 ACR/EULAR classification criteria. Results: We identified 300 children with Sjögren syndrome. The majority of patients n = 232 (77%) did not meet 2016 ACR/EULAR classification criteria, but n = 110 (37%) did not have sufficient testing done to even possibly achieve the score necessary to meet criteria. Even among those children with all criteria items tested, only 36% met criteria. The most common non-sicca symptoms were arthralgia [n = 161 (54%)] and parotitis [n = 140 (47%)] with parotitis inversely correlating with age. Conclusion: Sjögren syndrome in children can present at any age. Recurrent or persistent parotitis and arthralgias are common symptoms that should prompt clinicians to consider the possibility of Sjögren syndrome. The majority of children diagnosed with Sjögren syndromes did not meet 2016 ACR/EULAR classification criteria. Comprehensive diagnostic testing from the 2016 ACR/EULAR criteria are not universally performed. This may lead to under-recognition and emphasizes a need for further research including creation of paediatric-specific classification criteria.-
Descrição: dc.descriptionDivision of Pediatric Rheumatology Department of Pediatric and Adolescent Medicine Mayo Clinic-
Descrição: dc.descriptionDivision of Rheumatology Department of Pediatrics University of Utah School of Medicine-
Descrição: dc.descriptionDivision of Rheumatology The Children's Hospital of Philadelphia-
Descrição: dc.descriptionDepartment of Internal Medicine and Pediatrics The University of Chicago Medical Center-
Descrição: dc.descriptionDepartment of Pediatrics Duke University School of Medicine-
Descrição: dc.descriptionDepartment of Pediatrics Hematology and Oncology Medical University of Gdansk-
Descrição: dc.descriptionChildren's Mercy Hospital University of Missouri-Kansas City-
Descrição: dc.descriptionDivision of Rheumatology Irccs Ospedale Pediatrico Bambino Gesù-
Descrição: dc.descriptionDepartment of Pediatric Rheumatology Institute of Rheumatology-
Descrição: dc.descriptionDepartment of Pediatrics Columbia University Medical Center-
Descrição: dc.descriptionDivision of Rheumatology Children's National Hospital George Washington University School of Medicine and Health Sciences-
Descrição: dc.descriptionNational Institutes of Health National Institute of Arthritis and Musculoskeletal and Skin Diseases-
Descrição: dc.descriptionDepartment of Pediatrics University of Texas McGovern Medical School at Houston-
Descrição: dc.descriptionDivision of Pediatric Rheumatology Children's Healthcare of Atlanta Emory University School of Medicine-
Descrição: dc.descriptionInstituto de Puericultura e Pediatria Martagão Gesteira Universidade Federal Do Rio de Janeiro-
Descrição: dc.descriptionPediatric Rheumatology Hospital Sant Joan de Déu-
Descrição: dc.descriptionUniversitat de Barcelona Barcelona-
Descrição: dc.descriptionRheumatology Unit Department of Medicine School of Medical Science University of Campinas-
Descrição: dc.descriptionDivision of Rheumatology Department of Pediatrics University of Indiana School of Medicine Riley Hospital for Children at Indiana University Health-
Descrição: dc.descriptionPediatric Rheumatology Unit São Paulo State University (UNESP), Botucatu-
Descrição: dc.descriptionRheumatology Service Royal Children's Hospital Melbourne and Murdoch Children's Research Institute-
Descrição: dc.descriptionDivision of Pediatric Allergy Immunology and Rheumatology Department of Pediatrics College of Medicine University of Florida-
Descrição: dc.descriptionDivision of Oral Medicine Department of Oral and Maxillofacial Diagnostic Sciences College of Dentistry University of Florida-
Descrição: dc.descriptionRheumatology Department Hospital General Universitario Gregorio Marañón-
Descrição: dc.descriptionDivision of Immunology Boston Children's Hospital Department of Pediatrics Harvard Medical School-
Descrição: dc.descriptionDepartment of Rheumatic Diseases Tokyo Metropolitan Tama Medical Center-
Descrição: dc.descriptionDivision of Rheumatology Allergy and Immunology Stead Family Department of Pediatrics Carver College of Medicine University of Iowa-
Descrição: dc.descriptionPediatric Rheumatology Unit São Paulo State University (UNESP), Botucatu-
Formato: dc.format3144-3155-
Idioma: dc.languageen-
Relação: dc.relationRheumatology (United Kingdom)-
???dc.source???: dc.sourceScopus-
Palavras-chave: dc.subjectchildhood Sjögren syndrome-
Palavras-chave: dc.subjectpediatric rheumatology-
Palavras-chave: dc.subjectrecurrent parotitis-
Palavras-chave: dc.subjectSjögren Syndrome-
Título: dc.titleChildhood Sjögren syndrome: Features of an international cohort and application of the 2016 ACR/EULAR classification criteria-
Tipo de arquivo: dc.typelivro digital-
Aparece nas coleções:Repositório Institucional - Unesp

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