Consensus-based recommendations for the management of juvenile systemic sclerosis

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MetadadosDescriçãoIdioma
Autor(es): dc.contributorSchoen Clinic-
Autor(es): dc.contributorUniversity of Padova-
Autor(es): dc.contributorUniversity of Barcelona-
Autor(es): dc.contributorUniversity Children's Hospital-
Autor(es): dc.contributorAlder Hey Children's NHS Foundation Trust-
Autor(es): dc.contributorUniversity of Adelaide-
Autor(es): dc.contributorChildren's Hospital Westmead-
Autor(es): dc.contributorSemmelweis Hospital-
Autor(es): dc.contributorIstanbul University-Cerrahpasa-
Autor(es): dc.contributorUniversidade Federal do Rio de Janeiro (UFRJ)-
Autor(es): dc.contributorInstitute of Child Health University College London-
Autor(es): dc.contributorWilhelmina Children's Hospital-
Autor(es): dc.contributorUniversidade Estadual Paulista (UNESP)-
Autor(es): dc.contributorEuropean Reference Network RITA-
Autor(es): dc.creatorFoeldvari, Ivan-
Autor(es): dc.creatorCulpo, Roberta-
Autor(es): dc.creatorSperotto, Francesca-
Autor(es): dc.creatorAnton, Jordi-
Autor(es): dc.creatorAvcin, Tadej-
Autor(es): dc.creatorBaildam, Eileen-
Autor(es): dc.creatorBoros, Christina-
Autor(es): dc.creatorChaitow, Jeffrey-
Autor(es): dc.creatorConstantin, Tamas-
Autor(es): dc.creatorKasapcopur, Ozgur-
Autor(es): dc.creatorKnupp Feitosa De Oliveira, Sheila-
Autor(es): dc.creatorPilkington, Clarissa-
Autor(es): dc.creatorToplak, Natasa-
Autor(es): dc.creatorVan Royen, Annet-
Autor(es): dc.creatorSaad Magalhaes, Claudia-
Autor(es): dc.creatorVastert, Sebastiaan J-
Autor(es): dc.creatorWulffraat, Nico-
Autor(es): dc.creatorZulian, Francesco-
Data de aceite: dc.date.accessioned2025-08-21T19:56:36Z-
Data de disponibilização: dc.date.available2025-08-21T19:56:36Z-
Data de envio: dc.date.issued2022-04-29-
Data de envio: dc.date.issued2022-04-29-
Data de envio: dc.date.issued2021-04-01-
Fonte completa do material: dc.identifierhttp://dx.doi.org/10.1093/rheumatology/keaa584-
Fonte completa do material: dc.identifierhttp://hdl.handle.net/11449/228927-
Fonte: dc.identifier.urihttp://educapes.capes.gov.br/handle/11449/228927-
Descrição: dc.descriptionJuvenile systemic sclerosis (JSSc) is a rare disease of childhood and currently no international consensus exists with regard to its assessment and treatment. This SHARE (Single Hub and Access point for paediatric Rheumatology in Europe) initiative, based on expert opinion informed by the best available evidence, provides recommendations for the assessment and treatment of patients with JSSc with a view to improving their outcome. Experts focused attention not only on the skin assessment but also on the early signs of internal organ involvement whose proper treatment can significantly affect the long-term outcome. A score for disease severity is proposed in order to perform a structured assessment of outcome over time but a validation in a wider patient population is recommended. Finally, a stepwise treatment approach is proposed in order to unify the standard of care throughout Europe with the aim to reduce morbidity and mortality in this disease.-
Descrição: dc.descriptionHamburger Zentrum für Kinder- und Jugendrheumatologie Schoen Clinic-
Descrição: dc.descriptionDepartment of Woman and Child Health University of Padova, Via Giustiniani 3-
Descrição: dc.descriptionHospital Sant Joan de Déu University of Barcelona-
Descrição: dc.descriptionDepartment of Allergy Rheumatology and Clinical Immunology University Children's Hospital-
Descrição: dc.descriptionClinical and Academic Paediatric and Adolescent Rheumatology Unit Alder Hey Children's NHS Foundation Trust-
Descrição: dc.descriptionRheumatology Women's and Children's Hospital University of Adelaide-
Descrição: dc.descriptionRheumatology Children's Hospital Westmead-
Descrição: dc.descriptionDepartment of Pediatrics Semmelweis Hospital-
Descrição: dc.descriptionDepartment of Pediatrics Cerrahpasa Medical School Istanbul University-Cerrahpasa-
Descrição: dc.descriptionPediatric Rheumatology Unit Instituto de Puericultura e Pediatria Martagão Gesteira Universidade Federal Do Rio de Janeiro-
Descrição: dc.descriptionCentre for Adolescent Rheumatology Institute of Child Health University College London-
Descrição: dc.descriptionPaediatric Immunology and Rheumatology Wilhelmina Children's Hospital-
Descrição: dc.descriptionDepartment of Paediatrics Faculdade de Medicina de Botucatu-
Descrição: dc.descriptionDepartment of Paediatric Rheumatology Wilhelmina Children's Hospital-
Descrição: dc.descriptionEuropean Reference Network RITA-
Descrição: dc.descriptionDepartment of Paediatrics Faculdade de Medicina de Botucatu-
Formato: dc.format1651-1658-
Idioma: dc.languageen-
Relação: dc.relationRheumatology (Bulgaria)-
???dc.source???: dc.sourceScopus-
Palavras-chave: dc.subjectassessment-
Palavras-chave: dc.subjectjuvenile systemic sclerosis-
Palavras-chave: dc.subjectoutcome-
Palavras-chave: dc.subjectrecommendations-
Palavras-chave: dc.subjectscleroderma-
Palavras-chave: dc.subjectseverity score-
Palavras-chave: dc.subjecttreatment-
Título: dc.titleConsensus-based recommendations for the management of juvenile systemic sclerosis-
Tipo de arquivo: dc.typelivro digital-
Aparece nas coleções:Repositório Institucional - Unesp

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