Craniofacial Features in Richieri-Costa-Pereira Syndrome

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MetadadosDescriçãoIdioma
Autor(es): dc.contributorUniversidade de São Paulo (USP)-
Autor(es): dc.contributorUniversidade Estadual Paulista (UNESP)-
Autor(es): dc.creatorPardo, Milena P.-
Autor(es): dc.creatorSantos, Gabriela Lopes dos-
Autor(es): dc.creatorCarvalho, Izabel M.M.-
Autor(es): dc.creatorTjioe, Kellen Cristine-
Data de aceite: dc.date.accessioned2025-08-21T17:23:04Z-
Data de disponibilização: dc.date.available2025-08-21T17:23:04Z-
Data de envio: dc.date.issued2022-04-29-
Data de envio: dc.date.issued2022-04-29-
Data de envio: dc.date.issued2021-10-31-
Fonte completa do material: dc.identifierhttp://dx.doi.org/10.1177/1055665620987749-
Fonte completa do material: dc.identifierhttp://hdl.handle.net/11449/228900-
Fonte: dc.identifier.urihttp://educapes.capes.gov.br/handle/11449/228900-
Descrição: dc.descriptionObjective: Patients with Richieri-Costa-Pereira syndrome (RCPS) present severe craniofacial alterations and frequently require orthodontic and surgical procedures. Thus, this study aims to describe the craniofacial relationships in patients with RCPS. Design: Panoramic radiographs and lateral cephalometric teleradiographs of 7 patients with RCPS and 7 age- and sex-matched nonsyndromic patients were analyzed. Cephalometric measurements were used to determine the size of apical bases, the relationship between them, the pattern of craniofacial growth, and the facial heights of the patients. Interobservers’ concordance was verified by intraclass coefficient. For comparison between the groups, paired t test was employed. P values <.05 indicated statistical significance. Results: Average age of patients with RCPS was 18.5 years. Six patients were female. All patients with RCPS had Pierre-Robin sequence while 2 also presented cleft mandible. Most patients with RCPS had missing lower central incisors (100%), lower lateral incisors (85.7%), lower second premolars (85.7%), and/or upper lateral incisors (57.1%). Concordance between observers was excellent for all cephalometric measurements (0.87-0.99). Patients with RCPS presented severe craniofacial alterations when compared to control group: sella–nasion–B point (SNB) angle (73.8o ± 4.86o vs 78.85o ± 4.53o, P =.029), maxillary length (7.89 cm ± 0.58 cm vs 16.36 cm ± 0.75 cm, P =.001), mandibular length (9.90 cm ± 0.46 cm vs 20.61 cm ± 0.45 cm, P =.001), upper anterior face height (5.41 cm ± 0.50 cm vs 9.40 cm ± 0.47 cm, P =.001), lower anterior face height (5.48 cm ± 0.75 cm vs 11.66 cm ± 0.55 cm, P =.001), and posterior face height (6.70 cm ± 0.33 cm vs 13.65 cm ± 1.06 cm, P =.001). There was no difference in SNB, A point–nasion–B point, pogonion–nasion–B point, and mandibular place angles between the groups (P >.05). Conclusion: Patients with RCPS present deficient development of maxilla and mandible when compared with nonsyndromic patients.-
Descrição: dc.descriptionHospital for Rehabilitation of Craniofacial Anomalies University of São Paulo, Rua Silvio Marchione-
Descrição: dc.descriptionOral Oncology Center São Paulo State University, Rua Jose Bonifácio-
Descrição: dc.descriptionOral Oncology Center São Paulo State University, Rua Jose Bonifácio-
Formato: dc.format1370-1375-
Idioma: dc.languageen-
Relação: dc.relationCleft Palate-Craniofacial Journal-
???dc.source???: dc.sourceScopus-
Palavras-chave: dc.subjectcephalometry-
Palavras-chave: dc.subjectorthodontic treatment-
Palavras-chave: dc.subjectorthognathic surgery-
Palavras-chave: dc.subjectPierre-Robin sequence-
Palavras-chave: dc.subjectRichieri-Costa-Pereira syndrome-
Título: dc.titleCraniofacial Features in Richieri-Costa-Pereira Syndrome-
Tipo de arquivo: dc.typelivro digital-
Aparece nas coleções:Repositório Institucional - Unesp

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