Apresentação pediátrica da síndrome antifosfolípide

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MetadadosDescriçãoIdioma
Autor(es): dc.contributorUniversidade Estadual Paulista (UNESP)-
Autor(es): dc.creatorSato, Juliana de Oliveira-
Autor(es): dc.creatorde Carvalho, Simone Manso-
Autor(es): dc.creatorMagalhàes, Claudia Saad-
Data de aceite: dc.date.accessioned2025-08-21T15:15:38Z-
Data de disponibilização: dc.date.available2025-08-21T15:15:38Z-
Data de envio: dc.date.issued2022-04-28-
Data de envio: dc.date.issued2022-04-28-
Data de envio: dc.date.issued2008-12-01-
Fonte completa do material: dc.identifierhttp://hdl.handle.net/11449/225478-
Fonte: dc.identifier.urihttp://educapes.capes.gov.br/handle/11449/225478-
Descrição: dc.descriptionObjective: To describe clinical and laboratorial features as well as outcome in a paediatric series with defined diagnosis of antiphospholipid syndrome. Methods: A descriptive-retrospective report from a pediatric tertiary referral, with case ascertainment by vascular events identification, either venous thrombosis or arterial occlusion, anti-cardiolipin antibodies (IgG and IgM) titres and lupus anticoagulant tests. Results: Five cases, being two boys and three girls, were identified in the last five years. Venous thrombosis occurred in brain sinus vessels (2), fibular (2), popliteal (1), femoral (1), intestinal (1) and renal (1) veins, followed by arterial occlusion in the gut (1), kidneys (1) halux (1) this resulted in digit gangrene as a recurrent event occurring during warfarin treatment. A spontaneous abortion occurred in an adolescent with thrombocytopenic purpura evolving into haemolytic anemia (Evans Syndrome) and bleeding fatal outcome. Laboratory investigation resulted in at least one positive titre of IgG and/or IgM anticardiolipin antibodies in all of the cases, being considered as primary antiphospholipid syndrome. Three cases have been followed under oral anticoagulation treatment. Conclusion: Cerebral and extremities venous thrombosis were the most frequent events in this series. This points to early diagnosis and team approach for investigation and treatment.-
Descrição: dc.descriptionDepartamento de Pediatria Faculdade de Medicina de Botucatu Universidade Estadual Paulista (Unesp), 18618-970 Botucatu, SP-
Descrição: dc.descriptionDepartamento de Pediatria Faculdade de Medicina de Botucatu Universidade Estadual Paulista (Unesp), 18618-970 Botucatu, SP-
Formato: dc.format366-372-
Idioma: dc.languagept_BR-
Relação: dc.relationRevista Brasileira de Reumatologia-
???dc.source???: dc.sourceScopus-
Palavras-chave: dc.subjectAnticardiolipin antibodies-
Palavras-chave: dc.subjectAntiphospholipid syndrome-
Palavras-chave: dc.subjectEvans syndrome-
Palavras-chave: dc.subjectThrombosis-
Título: dc.titleApresentação pediátrica da síndrome antifosfolípide-
Título: dc.titlePaediatric antiphospholipid syndrome presentation-
Tipo de arquivo: dc.typelivro digital-
Aparece nas coleções:Repositório Institucional - Unesp

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